{"id":18701,"date":"2024-05-07T10:27:43","date_gmt":"2024-05-07T08:27:43","guid":{"rendered":"https:\/\/www.apo.com/magazin\/?post_type=ratgeber&#038;p=18701"},"modified":"2025-01-14T12:42:27","modified_gmt":"2025-01-14T11:42:27","slug":"ratgeber-mukoviszidose","status":"publish","type":"ratgeber","link":"https:\/\/www.apo.com/magazin\/ratgeber-mukoviszidose","title":{"rendered":"Mukoviszidose: Ursachen, Symptome und Behandlung"},"content":{"rendered":"<p><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-1 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: rgba(255,255,255,0);background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-0 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div class=\"fusion-text fusion-text-1\"><p>Mukoviszidose, auch als Zystische Fibrose bekannt, ist eine genetisch bedingte Erkrankung. Diese Krankheit betrifft vor allem die Lunge und das Verdauungssystem und kann zu schwerwiegenden Gesundheitsproblemen f\u00fchren. Doch was genau ist Mukoviszidose, welche Rolle spielt sie im K\u00f6rper und wie k\u00f6nnen Betroffene und ihre Familien mit dieser Erkrankung umgehen? In diesem Artikel erfahren Sie alles Wissenswerte \u00fcber Mukoviszidose, von den Ursachen bis zu den Behandlungsm\u00f6glichkeiten.<\/p>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-0{width:100% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-0 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 1.92%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-0{width:100% !important;order : 0;}.fusion-builder-column-0 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-0{width:100% !important;order : 0;}.fusion-builder-column-0 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-1{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-2 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: rgba(255,255,255,0);background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-1 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:24px;width:100%;\"><\/div><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:24px;width:100%;\"><\/div><div class=\"fusion-text fusion-text-2\"><h2><b><\/b>Mukoviszidose verstehen<\/h2>\n<\/div><div class=\"fusion-text fusion-text-3\"><p>Mukoviszidose ist eine erbliche Stoffwechselst\u00f6rung, die vor allem die Atemwege und das Verdauungssystem betrifft. Der Name &#8222;Mukoviszidose&#8220; leitet sich von den lateinischen <strong>Begriffen &#8222;mucus&#8220; f\u00fcr Schleim und &#8222;viscidus&#8220; f\u00fcr klebrig ab<\/strong>, was die Hauptmerkmale der Krankheit gut beschreibt. Sie ist durch eine St\u00f6rung im Salz- und Wassertransport durch die Zellmembranen verursacht,<strong> was zu einem z\u00e4hen, klebrigen Schleim <\/strong>f\u00fchrt. Dieser Schleim verstopft die Atemwege, die Bauchspeicheldr\u00fcse und andere Organe, was zu schwerwiegenden Komplikationen f\u00fchrt.<\/p>\n<p>Die Diagnose von Mukoviszidose erfolgt in Deutschland in den meisten F\u00e4llen <strong>in den ersten Lebensmonaten<\/strong>, da Mukoviszidose seit 2016 Bestandteil des Neugeborenen-Screenings ist. Bei \u00e4lteren Kindern k\u00f6nnen Symptome wie wiederkehrende Atemwegsinfektionen, Verdauungsprobleme oder Mangelern\u00e4hrung einen Hinweis auf die Erkrankung geben. In Deutschland werden jedes Jahr etwa 150 bis 200 Neugeborene mit Mukoviszidose diagnostiziert.<\/p>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-1{width:100% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-1 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 1.92%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-1{width:100% !important;order : 0;}.fusion-builder-column-1 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-1{width:100% !important;order : 0;}.fusion-builder-column-1 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-2{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-3 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: rgba(255,255,255,0);background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-2 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div class=\"fusion-text fusion-text-4\"><h2><strong>Was verursacht diese seltene Krankheit?<\/strong><\/h2>\n<\/div><div class=\"fusion-text fusion-text-5\"><p>Mukoviszidose ist eine genetische Erkrankung, was bedeutet, dass Kinder von ihren Eltern ein ver\u00e4ndertes Gen erben. Dieses Gen<strong>, auch bekannt als CFTR-Gen<\/strong> (Cystic Fibrosis Transmembrane Conductance Regulator), ist eine Einheit der im Erbgut von Lebewesen enthaltenen Erbinformation. Interessanterweise sind die Eltern in der Regel selbst nicht von der Krankheit betroffen. Allerdings tragen sie neben ihrer gesunden Erbanlage auch immer eine ver\u00e4nderte Version des Gens in sich. Die <strong>Wahrscheinlichkeit, dass ein Kind dieses Paares betroffen ist, betr\u00e4gt 1 zu 4<\/strong>, was bedeutet, dass es auch in einer Familie mehrere Kinder geben kann, die von der Krankheit betroffen sind.<\/p>\n<p>Die Mutation im CFTR-Gen f\u00fchrt dazu, dass das produzierte Protein nicht richtig funktioniert oder gar nicht produziert wird. Dadurch kann der Schleim in den Atemwegen und anderen betroffenen Organen zu dick und klebrig werden, was zu Entz\u00fcndungen, Infektionen und einer allm\u00e4hlichen Verschlechterung der Organfunktion f\u00fchrt.<\/p>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-2{width:100% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-2 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 1.92%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-2{width:100% !important;order : 0;}.fusion-builder-column-2 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-2{width:100% !important;order : 0;}.fusion-builder-column-2 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-3{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-4 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: #01063f;background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-3 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;background-color:#f4f4f4;padding: 20px 40px 20px 40px;\"><div class=\"fusion-text fusion-text-6\"><h3>Gut zu wissen<\/h3>\n<\/div><div class=\"fusion-text fusion-text-7\"><p>In Deutschland leben derzeit \u00fcber 8.000 Menschen mit dieser unheilbaren Krankheit. Interessanterweise ist jeder zwanzigste Deutsche Tr\u00e4ger des \u201eMukoviszidose-Gens\u201c, bleibt jedoch selbst gesund.<\/p>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-3{width:100% !important;margin-top : 0px;margin-bottom : 0px;}.fusion-builder-column-3 > .fusion-column-wrapper {padding-top : 20 !important;padding-right : 40 !important;margin-right : 1.92%;padding-bottom : 20 !important;padding-left : 40 !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-3{width:100% !important;}.fusion-builder-column-3 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-3{width:100% !important;}.fusion-builder-column-3 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-4{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-5 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: rgba(255,255,255,0);background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-4 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:12px;margin-bottom:12px;width:100%;\"><\/div><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:12px;margin-bottom:12px;width:100%;\"><\/div><div class=\"fusion-text fusion-text-8\"><h3>Welche Organe werden von Mukoviszidose betroffen?<\/h3>\n<p>Mukoviszidose betrifft in erster Linie die Atemwege und das Verdauungssystem, aber auch andere Organe k\u00f6nnen betroffen sein.<\/p>\n<ul>\n<li>Die Ansammlung von z\u00e4hem Schleim <strong>in den Atemwegen<\/strong> f\u00fchrt zu wiederkehrenden Atemwegsinfektionen, chronischem Husten, Atemnot und im fortgeschrittenen Stadium zu schweren Lungensch\u00e4den.<\/li>\n<li>Im <strong>Verdauungstrakt<\/strong> kann der z\u00e4he Schleim den Fluss von Verdauungsenzymen behindern, was zu Verdauungsst\u00f6rungen, Bauchschmerzen, Bl\u00e4hungen, Durchfall oder Fettst\u00fchlen f\u00fchrt. Dies kann zu N\u00e4hrstoffmangel, Gewichtsverlust und Wachstumsst\u00f6rungen f\u00fchren.<\/li>\n<li><strong>Die Bauchspeicheldr\u00fcse<\/strong> produziert Verdauungsenzyme, die f\u00fcr die Aufspaltung von Nahrungsmitteln erforderlich sind. Bei Menschen mit Mukoviszidose kann der z\u00e4he Schleim den Abfluss dieser Enzyme blockieren, was zu einer unzureichenden Verdauung von Nahrungsmitteln und einer Malabsorption (gest\u00f6rte N\u00e4hrstoffaufnahme) f\u00fchrt. Dadurch werden N\u00e4hrstoffe wie Fette, Proteine und Vitamine nicht richtig verdaut und absorbiert.<\/li>\n<li>Mukoviszidose kann sich auch <strong>auf die Leber auswirken<\/strong>, da der gestaute Schleim die Gallenwege blockieren kann, was zu Lebererkrankungen wie Gallensteine oder Leberzirrhose (fortgeschrittene Lebersch\u00e4digung) f\u00fchren kann.<\/li>\n<\/ul>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-4{width:100% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-4 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 1.92%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-4{width:100% !important;order : 0;}.fusion-builder-column-4 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-4{width:100% !important;order : 0;}.fusion-builder-column-4 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-5{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-6 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: rgba(255,255,255,0);background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-5 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div class=\"fusion-text fusion-text-9\"><h2>Symptome von Mukoviszidose<\/h2>\n<p>Die Symptome von Mukoviszidose k\u00f6nnen variieren und h\u00e4ngen oft davon ab, welches Organ am st\u00e4rksten betroffen ist. Zu den h\u00e4ufigsten Symptomen geh\u00f6ren:<\/p>\n<ul>\n<li><strong>Chronischer Husten und Atemprobleme:<\/strong> Aufgrund des z\u00e4hen Schleims in den Atemwegen haben Menschen mit Mukoviszidose oft Schwierigkeiten beim Atmen. Chronischer Husten, wiederkehrende Lungenentz\u00fcndungen und Atemnot sind h\u00e4ufige Probleme.<\/li>\n<li><strong>Verdauungsprobleme:<\/strong> Der z\u00e4he Schleim kann auch den Verdauungstrakt beeintr\u00e4chtigen, was zu Problemen wie Verdauungsst\u00f6rungen, Bauchschmerzen, Durchfall oder Fettst\u00fchlen f\u00fchrt. Dies kann zu Mangelern\u00e4hrung und Wachstumsst\u00f6rungen bei Kindern f\u00fchren.<\/li>\n<li><strong>Gewichtsverlust und Unterern\u00e4hrung:<\/strong> Aufgrund der Verdauungsprobleme und der schlechten N\u00e4hrstoffaufnahme k\u00f6nnen Menschen mit Mukoviszidose Schwierigkeiten haben, ein normales K\u00f6rpergewicht zu halten. Dies kann zu einem Mangel an wichtigen N\u00e4hrstoffen f\u00fchren und das Risiko von Komplikationen erh\u00f6hen.<\/li>\n<li><strong>Infektionen:<\/strong> Die Ansammlung von Schleim in den Atemwegen schafft ein ideales Umfeld f\u00fcr das Wachstum von Bakterien und anderen Krankheitserregern. Dadurch sind Menschen mit Mukoviszidose anf\u00e4lliger f\u00fcr wiederkehrende Atemwegsinfektionen wie Bronchitis und Lungenentz\u00fcndung.<\/li>\n<\/ul>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-5{width:100% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-5 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 1.92%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-5{width:100% !important;order : 0;}.fusion-builder-column-5 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-5{width:100% !important;order : 0;}.fusion-builder-column-5 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-6{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-7 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: rgba(255,255,255,0);background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-6 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div class=\"fusion-text fusion-text-10\"><h2>Diagnose von Mukoviszidose<\/h2>\n<p>In den meisten F\u00e4llen wird die Krankheit bereits im S\u00e4uglings- oder Kleinkindalter diagnostiziert, aber sie kann auch sp\u00e4ter im Leben diagnostiziert werden, insbesondere wenn die Symptome mild sind oder sich langsam entwickeln.<\/p>\n<p>In der Regel wird Mukoviszidose durch das Neugeborenen-Screening erkannt, das fl\u00e4chendeckend in Deutschland angeboten wird. Dabei entnimmt ein Arzt oder eine \u00c4rztin dem Neugeborenen am 2. bis 3. Lebenstag Blut aus der Ferse.Die vollst\u00e4ndige Diagnose von Mukoviszidose erfolgt durch eine<strong> Kombination aus klinischen Symptomen, genetischen Tests und speziellen Untersuchungen<\/strong>.<\/p>\n<p>Die vollst\u00e4ndige Diagnose von Mukoviszidose erfolgt durch eine<strong> Kombination aus klinischen Symptomen, genetischen Tests und speziellen Untersuchungen<\/strong>.<\/p>\n<p>Die Hauptuntersuchung in der Diagnostik der Mukoviszidose ist die Durchf\u00fchrung eines Schwei\u00dftests. Liegt das Ergebnis des Schwei\u00dftests im Graubereich oder best\u00e4tigt ein positives Ergebnis den Verdacht auf Mukoviszidose, wird ein genetischer Test durchgef\u00fchrt. Die genetischen Tests zielen darauf ab, die Mutationen im CFTR-Gen zu identifizieren, was u.a. wichtig ist f\u00fcr die sp\u00e4tere Therapie. \u00a0Dar\u00fcber hinaus k\u00f6nnen verschiedene Tests durchgef\u00fchrt werden, um die Funktion der Lunge, des Verdauungssystems und anderer betroffener Organe zu \u00fcberpr\u00fcfen. Dazu geh\u00f6ren Lungenfunktionstestsund bildgebende Verfahren.<\/p>\n<p>Detaillierte Informationen zur Diagnose der Mukoviszidose, u.a. ein Video zur Erkl\u00e4rung des Schwei\u00dftests, <a href=\"https:\/\/www.muko.info\/mukoviszidose\/diagnostik\">gibt es auf der Seite des Mukoviszidose e.V..<\/a><\/p>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-6{width:100% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-6 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 1.92%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-6{width:100% !important;order : 0;}.fusion-builder-column-6 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-6{width:100% !important;order : 0;}.fusion-builder-column-6 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-7{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-8 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: #01063f;background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-7 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;background-color:#f4f4f4;padding: 20px 40px 20px 40px;\"><div class=\"fusion-text fusion-text-11\"><h3>Gut zu wissen<\/h3>\n<\/div><div class=\"fusion-text fusion-text-12\"><p>Die fr\u00fchzeitige Diagnose von Mukoviszidose ist entscheidend, um eine angemessene Behandlung und Betreuung zu erm\u00f6glichen und das Fortschreiten der Krankheit zu verlangsamen. In den n\u00e4chsten Abschnitten werden wir uns genauer mit den Behandlungsm\u00f6glichkeiten und der Lebensqualit\u00e4t von Menschen mit Mukoviszidose befassen.<\/p>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-7{width:100% !important;margin-top : 0px;margin-bottom : 0px;}.fusion-builder-column-7 > .fusion-column-wrapper {padding-top : 20 !important;padding-right : 40 !important;margin-right : 1.92%;padding-bottom : 20 !important;padding-left : 40 !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-7{width:100% !important;}.fusion-builder-column-7 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-7{width:100% !important;}.fusion-builder-column-7 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-8{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-9 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: rgba(255,255,255,0);background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-8 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:12px;margin-bottom:12px;width:100%;\"><\/div><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:12px;margin-bottom:12px;width:100%;\"><\/div><div class=\"fusion-text fusion-text-13\"><h2>Therapie von Mukoviszidose<\/h2>\n<p>Die Behandlung von Mukoviszidose umfasst verschiedene Ma\u00dfnahmen, um die Symptome zu lindern, Komplikationen zu verhindern und die Lebensqualit\u00e4t zu verbessern. Dazu geh\u00f6ren:<\/p>\n<ul>\n<li><strong>Medikament\u00f6se Therapie:<\/strong> Mukolytika werden eingesetzt, um den z\u00e4hen Schleim zu l\u00f6sen und das Abhusten zu erleichtern. Bronchodilatatoren helfen dabei, die Atemwege zu erweitern und die Atmung zu erleichtern. Spezielle Medikamente namens CFTR-Modulatoren zielen darauf ab, die Funktionsst\u00f6rung des CFTR-Gens teilweise auszugleichen, indem sie die Ver\u00e4nderungen in den Zellen des K\u00f6rpers beeinflussen. Antibiotika werden verwendet, um Infektionen zu behandeln und zu verhindern. Inhalationen mit Salz NaCl (Natriumchlorid) und Bronchodilatatoren wie Salbutamol sowie Dornase alpha helfen, die Konsistenz des Schleims zu ver\u00e4ndern, sodass er leichter abgehustet werden kann.<\/li>\n<li><strong>Physiotherapie:<\/strong> Verschiedene Atem\u00fcbungen und -techniken helfen, den Schleim aus den Atemwegen zu entfernen, die Lungenfunktion zu verbessern und Infektionen vorzubeugen. Dazu geh\u00f6ren auch Verneblertherapie, PEP (Positive-Expiratory-Pressure)-Masken und Vibrationsger\u00e4te, die dabei helfen, den Schleim abzuhusten. Neben Atemwegstechniken werden auch autogene Drainage und andere Methoden eingesetzt, um die Atemwege frei zu halten und die Lungenfunktion zu unterst\u00fctzen.<\/li>\n<li><strong>Ern\u00e4hrungstherapie:<\/strong> Eine angepasste Ern\u00e4hrung ist wichtig, um den N\u00e4hrstoffbedarf zu decken und das Gewicht zu halten. Dies kann die Einnahme von Enzymersatzpr\u00e4paraten zur Unterst\u00fctzung der Verdauung und hochkalorische Nahrungssupplementierung beinhalten. Zudem m\u00fcssen fettl\u00f6sliche Vitamine wie A, D, E und K substituiert werden. Eine erh\u00f6hte Fl\u00fcssigkeitszufuhr unterst\u00fctzt ebenfalls die Schleiml\u00f6sung und -ausscheidung.<\/li>\n<\/ul>\n<p>Obwohl Mukoviszidose derzeit noch nicht heilbar ist, haben Fortschritte in der medizinischen Forschung und Behandlung die Lebenserwartung und Lebensqualit\u00e4t der Betroffenen in den letzten Jahrzehnten erheblich verbessert<strong>. Fr\u00fchzeitige Diagnose, multidisziplin\u00e4re Betreuung und die Entwicklung neuer Therapien<\/strong> geben Hoffnung auf eine bessere Zukunft f\u00fcr Menschen, die mit dieser herausfordernden Erkrankung leben.<\/p>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-8{width:100% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-8 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 1.92%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-8{width:100% !important;order : 0;}.fusion-builder-column-8 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-8{width:100% !important;order : 0;}.fusion-builder-column-8 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-9{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-10 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: #01063f;background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-9 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;background-color:#f4f4f4;padding: 20px 40px 20px 40px;\"><iframe width=\"560\" height=\"315\" src=\"https:\/\/www.youtube.com\/embed\/X_BR_AwohEw?si=NwHTGY4nSSrL9HHF\" title=\"YouTube video player\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" allowfullscreen><\/iframe><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:24px;width:100%;\"><\/div><iframe width=\"560\" height=\"315\" src=\"https:\/\/www.youtube.com\/embed\/YJpUQ6n0bUI?si=QJu0apHrLrKu535U\" title=\"YouTube video player\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" allowfullscreen><\/iframe><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-9{width:100% !important;margin-top : 0px;margin-bottom : 0px;}.fusion-builder-column-9 > .fusion-column-wrapper {padding-top : 20 !important;padding-right : 40 !important;margin-right : 1.92%;padding-bottom : 20 !important;padding-left : 40 !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-9{width:100% !important;}.fusion-builder-column-9 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-9{width:100% !important;}.fusion-builder-column-9 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-10{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-11 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: rgba(255,255,255,0);background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-10 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:12px;margin-bottom:12px;width:100%;\"><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-10{width:100% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-10 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 1.92%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-10{width:100% !important;order : 0;}.fusion-builder-column-10 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-10{width:100% !important;order : 0;}.fusion-builder-column-10 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-11{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-12 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: rgba(255,255,255,0);background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-11 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><style type=\"text\/css\">.fusion-accordian  #accordion-18701-1 .panel-title a .fa-fusion-box{ color: #ffffff;}.fusion-accordian  #accordion-18701-1 .panel-title a .fa-fusion-box:before{ font-size: 16px; width: 16px;}.fusion-accordian  #accordion-18701-1 .panel-title a{font-size:28px;}.fusion-accordian  #accordion-18701-1 .fa-fusion-box { background-color: #212934;border-color: #212934;}.fusion-accordian  #accordion-18701-1 .panel-title a:hover, #accordion-18701-1 .fusion-toggle-boxed-mode:hover .panel-title a { color: #65bc7b;}.fusion-accordian  #accordion-18701-1 .panel-title .active .fa-fusion-box,.fusion-accordian  #accordion-18701-1 .panel-title a:hover .fa-fusion-box { background-color: #65bc7b!important;border-color: #65bc7b!important;}<\/style><div class=\"accordian fusion-accordian\"><div class=\"panel-group\" id=\"accordion-18701-1\"><div class=\"fusion-panel panel-default\"><div class=\"panel-heading\"><h4 class=\"panel-title toggle\"><a aria-expanded=\"false\" aria-controls=\"7d819a0663821d76b\" role=\"button\" data-toggle=\"collapse\" data-parent=\"#accordion-18701-1\" data-target=\"#7d819a0663821d76b\" href=\"#7d819a0663821d76b\"><span class=\"fusion-toggle-icon-wrapper\" aria-hidden=\"true\"><i class=\"fa-fusion-box\" aria-hidden=\"true\"><\/i><\/span><span class=\"fusion-toggle-heading\">Quellen<\/span><\/a><\/h4><\/div><div id=\"7d819a0663821d76b\" class=\"panel-collapse collapse \"><div class=\"panel-body toggle-content fusion-clearfix\">\n<ul>\n<li><a href=\"https:\/\/www.muko.info\/\">Mukoviszidose e.V. &#8211; Bundesverband Cystische Fibrose (CF) | Mukoviszidose e.V. Bundesverband Cystische Fibrose (CF)<\/a><\/li>\n<li><a href=\"https:\/\/patienten-information.de\/kurzinformationen\/mukoviszidose\">https:\/\/patienten-information.de\/kurzinformationen\/mukoviszidose<\/a><\/li>\n<li><a href=\"https:\/\/flexikon.doccheck.com\/de\/Mukoviszidose\">https:\/\/flexikon.doccheck.com\/de\/Mukoviszidose<\/a><\/li>\n<li><a href=\"https:\/\/www.muko.info\/mukoviszidose\/ueber-die-erkrankung#:~:text=Mukoviszidose%20ist%20eine%20angeborene%20Stoffwechselerkrankung,viscidus%E2%80%9C%20(z%C3%A4h)%20zusammen\">https:\/\/www.muko.info\/mukoviszidose\/ueber-die-erkrankung#:~:text=Mukoviszidose%20ist%20eine%20angeborene%20Stoffwechselerkrankung,viscidus%E2%80%9C%20(z%C3%A4h)%20zusammen<\/a>.<\/li>\n<\/ul>\n<\/div><\/div><\/div><\/div><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-11{width:100% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-11 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 1.92%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-11{width:100% !important;order : 0;}.fusion-builder-column-11 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-11{width:100% !important;order : 0;}.fusion-builder-column-11 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-12{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-13 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"background-color: rgba(255,255,255,0);background-position: center center;background-repeat: no-repeat;border-width: 0px 0px 0px 0px;border-color:#e2e2e2;border-style:solid;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-center\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-12 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div class=\"fusion-text fusion-text-14\"><h3><strong>Gepr\u00fcft durch unser pharmazeutisches Team<\/strong><\/h3>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-12{width:100% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-12 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 1.92%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-12{width:100% !important;order : 0;}.fusion-builder-column-12 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-12{width:100% !important;order : 0;}.fusion-builder-column-12 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-13 fusion_builder_column_1_5 1_5 fusion-flex-column fusion-flex-align-self-flex-start\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-center fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div ><span class=\" fusion-imageframe imageframe-none imageframe-1 hover-type-none\"><img decoding=\"async\" width=\"1200\" height=\"1200\" alt=\"Felix Hoffman, pharmazeutischer Experte\" title=\"Felix Hoffman\" src=\"https:\/\/www.apo.com/magazin\/wp-content\/uploads\/2024\/05\/51.jpg\" class=\"img-responsive wp-image-19286\" srcset=\"https:\/\/www.apo.com/magazin\/wp-content\/uploads\/2024\/05\/51-200x200.jpg 200w, https:\/\/www.apo.com/magazin\/wp-content\/uploads\/2024\/05\/51-400x400.jpg 400w, https:\/\/www.apo.com/magazin\/wp-content\/uploads\/2024\/05\/51-600x600.jpg 600w, https:\/\/www.apo.com/magazin\/wp-content\/uploads\/2024\/05\/51-800x800.jpg 800w, https:\/\/www.apo.com/magazin\/wp-content\/uploads\/2024\/05\/51.jpg 1200w\" sizes=\"(max-width: 640px) 100vw, 200px\" \/><\/span><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-13{width:20% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-13 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 9.6%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 9.6%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-13{width:20% !important;order : 0;}.fusion-builder-column-13 > .fusion-column-wrapper {margin-right : 9.6%;margin-left : 9.6%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-13{width:100% !important;order : 0;}.fusion-builder-column-13 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-14 fusion_builder_column_4_5 4_5 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div class=\"fusion-text fusion-text-15\"><p>\u201e<i><span data-contrast=\"auto\">An der Pharmazie fasziniert mich am meisten, wie alles zusammenspielt. Von Zusammenh\u00e4ngen im Stoffwechsel hin zur Einnahme von Medikamenten. Wer sich damit auskennt, kann sein Leben positiv beeinflussen.\u201c<\/span><\/i><span data-ccp-props=\"{\">\u00a0<\/span><\/p>\n<\/div><div class=\"fusion-text fusion-text-16\"><p><a href=\"https:\/\/de.linkedin.com\/in\/hoffmannfelix90\"><b><span data-contrast=\"none\">Felix Hoffmann<\/span><\/b><\/a>\u00a0<span data-contrast=\"auto\">lebt f\u00fcr die Pharmazie und bringt eine gro\u00dfe Expertise in der Beratung mit. Mit seinem fundierten Wissen garantiert er die hohen Qualit\u00e4tsstandards der pharmazeutischen Inhalte auf\u00a0<\/span><a href=\"https:\/\/www.apo.com\/\"><span data-contrast=\"none\">apo.com<\/span><\/a><span data-contrast=\"auto\">.<\/span><span data-ccp-props=\"{\">\u00a0<\/span><\/p>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-14{width:80% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-14 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 2.4%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 2.4%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-14{width:80% !important;order : 0;}.fusion-builder-column-14 > .fusion-column-wrapper {margin-right : 2.4%;margin-left : 2.4%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-14{width:100% !important;order : 0;}.fusion-builder-column-14 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-15 fusion_builder_column_1_1 1_1 fusion-flex-column\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\" style=\"background-position:left top;background-repeat:no-repeat;-webkit-background-size:cover;-moz-background-size:cover;-o-background-size:cover;background-size:cover;padding: 0px 0px 0px 0px;\"><div class=\"fusion-text fusion-text-17\"><div class=\"fusion-text fusion-text-17\"><\/div>\n<p>Wichtiger Hinweis: Unsere Artikel und Grafiken werden von unserem Expertenteam f\u00fcr chronische Erkrankungen \u00fcberpr\u00fcft. Grundlage sind stets seri\u00f6se Quellen, wissenschaftliche Artikel, Leitlinien und \u00e4rztliche Aussagen. Die Inhalte werden in regelm\u00e4\u00dfigen Abst\u00e4nden aktualisiert und dienen weder der Selbstdiagnose noch ersetzen sie einen Arztbesuch.<\/p>\n<\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-builder-column-15{width:100% !important;margin-top : 0px;margin-bottom : 20px;}.fusion-builder-column-15 > .fusion-column-wrapper {padding-top : 0px !important;padding-right : 0px !important;margin-right : 1.92%;padding-bottom : 0px !important;padding-left : 0px !important;margin-left : 1.92%;}@media only screen and (max-width:1024px) {.fusion-body .fusion-builder-column-15{width:100% !important;order : 0;}.fusion-builder-column-15 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}@media only screen and (max-width:640px) {.fusion-body .fusion-builder-column-15{width:100% !important;order : 0;}.fusion-builder-column-15 > .fusion-column-wrapper {margin-right : 1.92%;margin-left : 1.92%;}}<\/style><\/div><\/div><style type=\"text\/css\">.fusion-body .fusion-flex-container.fusion-builder-row-13{ padding-top : 0px;margin-top : 0px;padding-right : 0px;padding-bottom : 0px;margin-bottom : 0px;padding-left : 0px;}<\/style><\/div>\n<\/p>\n","protected":false},"excerpt":{"rendered":"","protected":false},"author":30,"featured_media":18756,"parent":0,"menu_order":0,"template":"","meta":{"_lmt_disableupdate":"no","_lmt_disable":"","footnotes":""},"categories":[77],"class_list":["post-18701","ratgeber","type-ratgeber","status-publish","has-post-thumbnail","hentry","category-weitere-themen"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.8 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Mukoviszidose: Ursachen, Symptome und Behandlung | apo.com Magazin<\/title>\n<meta name=\"description\" content=\"Fast alle zwei Tage wird ein Kind mit Mukoviszidose geboren. 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